2025 ICD-10-CM Diagnosis Code E84.0

Cystic fibrosis with pulmonary manifestations

• E84.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2025 edition of ICD-10-CM E84.0 became effective on October 1, 2024.
• This is the American ICD-10-CM version of E84.0 – other international versions of ICD-10 E84.0 may differ.

Use Additional

• code to identify any infectious organism present, such as:
• Pseudomonas (B96.5)

The following code(s) above E84.0 contain annotation back-references

 that may be applicable to E84.0:

• E00-E89  Endocrine, nutritional and metabolic diseases
• E70-E88  Metabolic disorders
• E84  Cystic fibrosis

Approximate Synonyms

• Cystic fibrosis of the lung
• Cystic fibrosis, pulmonary

ICD-10-CM E84.0 is grouped within Diagnostic Related Group(s) (MS-DRG v42.0):

• 177 Respiratory infections and inflammations with mcc
• 178 Respiratory infections and inflammations with cc
• 179 Respiratory infections and inflammations without cc/mcc

Convert E84.0 to ICD-9-CMCode History

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change
• 2024 (effective 10/1/2023): No change
• 2025 (effective 10/1/2024): No change

Code annotations containing back-references to E84.0:

• Code Also: I27.23
• Type 1 Excludes: J99, P78, Q33.0, Q45.3

Diagnosis Index entries containing back-references to E84.0:

• Fibrosis, fibrotic
  • cystic (of pancreas) E84.9
    • with
      • pulmonary manifestations E84.0