2025 ICD-10-CM Diagnosis Code E00.1

Congenital iodine-deficiency syndrome, myxedematous type

  • E00.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2025 edition of ICD-10-CM E00.1 became effective on October 1, 2024.
  • This is the American ICD-10-CM version of E00.1 – other international versions of ICD-10 E00.1 may differ.

Applicable To

  • Endemic hypothyroid cretinism
  • Endemic cretinism, myxedematous type

The following code(s) above E00.1 contain annotation back-references

 that may be applicable to E00.1:

  • E00-E89  Endocrine, nutritional and metabolic diseases
  • E00  Congenital iodine-deficiency syndrome

Approximate Synonyms

  • Congenital iodine deficiency syndrome, myxedematous ty
  • Endemic congenital iodine deficiency syndrome of myxedematous type

Clinical Information

  • Severely reduced physical and mental growth associated with pyramidal and extrapyramidal signs and symptoms, due to dietary iodine deficiency.

ICD-10-CM E00.1 is grouped within Diagnostic Related Group(s) (MS-DRG v42.0):

  • 643 Endocrine disorders with mcc
  • 644 Endocrine disorders with cc
  • 645 Endocrine disorders without cc/mcc

Convert E00.1 to ICD-9-CMCode History

  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
  • 2024 (effective 10/1/2023): No change
  • 2025 (effective 10/1/2024): No change

Code annotations containing back-references to E00.1:

  • Code First: G13.2

Diagnosis Index entries containing back-references to E00.1:

  • Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic) E00.9
    • type
      • hypothyroid E00.1
      • myxedematous E00.1
  • Myxedema (adult) (idiocy) (infantile) (juvenile) E03.9 – see also Hypothyroidism
    • congenital E00.1
  • Syndrome – see also Disease
    • iodine-deficiency, congenitalE00.9
      • type
        • myxedematous E00.1
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